Maurice van Steensel

All articles by Maurice van Steensel

Pachyonychia Congenita

Are You Confident of the Diagnosis? What should be alert for in the history A family history should be elicited, as well as any history of recurrent trauma or hobby-related chronic use of the hands and feet. Painful callusing on the feet is almost pathognomonic in a patient with keratoderma and thickened nails. Morning/starting pain…

Klippel-Trenaunay Syndrome (vascular malformation-deregulated growth syndrome[s], VM-DG type 3/Girth type/Klippel-Trenaunay type, KTS, Klipppel-Trenaunay-Weber, and angioosteohypertrophy syndrome

Are You Confident of the Diagnosis? What you should be alert for in the history As a rule, most people with Klippel-Trenaunay syndrome (KTS) are in good general health and will be able to deal adequately with their condition. At first presentation, there will usually not be specific complaints. A good history will suffice to…

Palmoplantar Keratodermas

Are You Confident of the Diagnosis? Palmoplantar keratodermas (hereby referred to as PPKs) represent a large, varied group of syndromes that are vastly different with respect to symptoms and clinical presentation. Please refer to Table I for syndrome names, synonyms. Images for the syndromes discussed are cited in the Evidence section at the end of…

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